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Academic Journal

Age- and sex-specific biomechanics and extracellular matrix remodeling of the ascending aorta in a mouse model of severe Marfan syndrome.

  • Authors : Dwivedi KK; Department of Mechanical Engineering and Materials Science, Washington University in St. Louis, St. Louis, Missouri, United States.; Rother J

Subjects: Marfan Syndrome*/Marfan Syndrome*/Marfan Syndrome*/complications ; Marfan Syndrome*/Marfan Syndrome*/Marfan Syndrome*/metabolism ; Marfan Syndrome*/Marfan Syndrome*/Marfan Syndrome*/physiopathology

  • Source: American journal of physiology. Heart and circulatory physiology [Am J Physiol Heart Circ Physiol] 2024 Oct 01; Vol. 327 (4), pp. H1037-H1051. Date of Electronic Publication: 2024 Publisher: American Physiological Society Country of Publication: United States NLM ID: 100901228 Publication Model: Print-Electronic Cited Medium:

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Academic Journal

Developmental abnormalities in the cornea of a mouse model for Marfan syndrome.

  • Authors : Feneck EM; Structural Biophysics Research Group, School of Optometry and Vision Sciences, Cardiff University, Maindy Road, Cardiff, CF24 4HQ, UK.; Souza RB

Subjects: Cornea/Cornea/Cornea/*abnormalities ; Extracellular Matrix/Extracellular Matrix/Extracellular Matrix/*metabolism ; Marfan Syndrome/Marfan Syndrome/Marfan Syndrome/*pathology

  • Source: Experimental eye research [Exp Eye Res] 2020 May; Vol. 194, pp. 108001. Date of Electronic Publication: 2020 Mar 13.Publisher: Academic Press Country of Publication: England NLM ID: 0370707 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Premature aortic smooth muscle cell differentiation contributes to matrix dysregulation in Marfan Syndrome.

  • Authors : Dale M; Department of Surgery, University of Nebraska Medical Center, Omaha, Nebraska, United States of America.; Fitzgerald MP

Subjects: Aorta, Thoracic/Aorta, Thoracic/Aorta, Thoracic/*pathology ; Aortic Aneurysm, Thoracic/Aortic Aneurysm, Thoracic/Aortic Aneurysm, Thoracic/*pathology ; Extracellular Matrix/Extracellular Matrix/Extracellular Matrix/*pathology

  • Source: PloS one [PLoS One] 2017 Oct 17; Vol. 12 (10), pp. e0186603. Date of Electronic Publication: 2017 Oct 17 (Print Publication: 2017).Publisher: Public Library of Science Country of Publication: United States NLM ID: 101285081 Publication Model: eCollection Cited Medium: Internet

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Academic Journal

IL-6 regulates extracellular matrix remodeling associated with aortic dilation in a fibrillin-1 hypomorphic mgR/mgR mouse model of severe Marfan syndrome.

  • Authors : Ju X; Department of Biochemistry and Molecular Biology, University of Texas Medical Branch, Galveston, TX.; Ijaz T

Subjects: Aorta/Aorta/Aorta/*metabolism ; Aortic Aneurysm, Thoracic/Aortic Aneurysm, Thoracic/Aortic Aneurysm, Thoracic/*etiology ; Extracellular Matrix/Extracellular Matrix/Extracellular Matrix/*metabolism

  • Source: Journal of the American Heart Association [J Am Heart Assoc] 2014 Jan 21; Vol. 3 (1), pp. e000476. Date of Electronic Publication: 2014 Jan 21.Publisher: Wiley-Blackwell Country of Publication: England NLM ID: 101580524 Publication Model: Electronic Cited Medium: Internet ISSN: 2047-9980

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Academic Journal

Bone lessons from Marfan syndrome and related disorders: fibrillin, TGF-B and BMP at the balance of too long and too short.

  • Authors : Loeys BL; Center for Medical Genetics, University of Antwerp, Antwerp, BE. ; Mortier G

Subjects: Bone Morphogenetic Proteins/Bone Morphogenetic Proteins/Bone Morphogenetic Proteins/*metabolism ; Extracellular Matrix/Extracellular Matrix/Extracellular Matrix/*metabolism ; Loeys-Dietz Syndrome/Loeys-Dietz Syndrome/Loeys-Dietz Syndrome/*physiopathology

  • Source: Pediatric endocrinology reviews : PER [Pediatr Endocrinol Rev] 2013 Jun; Vol. 10 Suppl 2, pp. 417-23.Publisher: Y.S. Medical Media Ltd Country of Publication: Israel NLM ID: 101202124 Publication Model: Print Cited Medium: Print ISSN: 1565-4753

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Academic Journal

Fell-Muir Lecture: Fibrillin microfibrils: structural tensometers of elastic tissues?

  • Authors : Kielty CM; Wellcome Trust Centre for Cell-Matrix Research, School of Biological Sciences, Faculty of Biology, Medicine and Health, University of Manchester, Manchester, UK.

Subjects: Elastic Tissue/Elastic Tissue/Elastic Tissue/*pathology ; Extracellular Matrix/Extracellular Matrix/Extracellular Matrix/*pathology ; Fibrillins/Fibrillins/Fibrillins/*metabolism

  • Source: International journal of experimental pathology [Int J Exp Pathol] 2017 Aug; Vol. 98 (4), pp. 172-190. Date of Electronic Publication: 2017 Sep 14.Publisher: Wiley Country of Publication: England NLM ID: 9014042 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1365-2613

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Academic Journal

Microfibrils: a cornerstone of extracellular matrix and a key to understand Marfan syndrome.

  • Authors : Bonetti MI; Department of Anatomy, Histology and Forensic Medicine, University of Florence, Italy.

Subjects: Extracellular Matrix/Extracellular Matrix/Extracellular Matrix/*metabolism ; Marfan Syndrome/Marfan Syndrome/Marfan Syndrome/*metabolism ; Microfibrils/Microfibrils/Microfibrils/*metabolism

  • Source: Italian journal of anatomy and embryology = Archivio italiano di anatomia ed embriologia [Ital J Anat Embryol] 2009 Oct-Dec; Vol. 114 (4), pp. 201-24.Publisher: Editrice Il Sedicesimo Country of Publication: Italy NLM ID: 9612303 Publication Model: Print Cited Medium: Print ISSN: 1122-6714

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Academic Journal

Genetic models of fibrillinopathies.

Subjects: BIOLOGICAL models; MARFAN syndrome; GENETIC mutation

  • Source: Genetics. Jan2024, Vol. 226 Issue 1, p1-19. 19p.

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Academic Journal

Glycoproteomic Analysis of the Aortic Extracellular Matrix in Marfan Patients.

  • Authors : Yin 殷晓科 X; From the King's British Heart Foundation Centre, King's College London, United Kingdom (X.Y., A.L.F., J.B.-B., R.L., M.F., F.B., P.S., Q.X., M.M.).; Wanga S

Subjects: Aorta/Aorta/Aorta/*chemistry ; Extracellular Matrix/Extracellular Matrix/Extracellular Matrix/*chemistry ; Glycopeptides/Glycopeptides/Glycopeptides/*analysis

  • Source: Arteriosclerosis, thrombosis, and vascular biology [Arterioscler Thromb Vasc Biol] 2019 Sep; Vol. 39 (9), pp. 1859-1873. Date of Electronic Publication: 2019 Jul 18.Publisher: Lippincott Williams & Wilkins Country of Publication: United States NLM ID: 9505803 Publication Model: Print-Electronic Cited Medium:

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Academic Journal

In vivo corneal confocal microscopy in marfan syndrome.

Subjects: Diagnostic Techniques, Ophthalmological* ; Microscopy, Confocal*; Cornea/Cornea/Cornea/*pathology

  • Source: Cornea [Cornea] 2007 Aug; Vol. 26 (7), pp. 787-92.Publisher: Lippincott Williams & Wilkins Country of Publication: United States NLM ID: 8216186 Publication Model: Print Cited Medium: Print ISSN:

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  • 1-10 of  597 results for ""MARFAN syndrome""