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Academic Journal

Growth and Body Composition in PKU Children-A Three-Year Prospective Study Comparing the Effects of L-Amino Acid to Glycomacropeptide Protein Substitutes.

  • Authors : Daly A; Birmingham Women's and Children's Hospital, NHS Foundation Trust, Birmingham B4 6NH, UK.; Högler W

Subjects: Amino Acids/Amino Acids/Amino Acids/*administration & dosage ; Body Composition/Body Composition/Body Composition/*drug effects ; Caseins/Caseins/Caseins/*administration & dosage

  • Source: Nutrients [Nutrients] 2021 Apr 16; Vol. 13 (4). Date of Electronic Publication: 2021 Apr 16.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Protein Substitutes in PKU; Their Historical Evolution.

  • Authors : Daly A; Birmingham Women's and Children's Hospital, NHS Foundation Trust, Birmingham B4 6NH, UK.; Evans S

Subjects: Phenylalanine*/Phenylalanine*/Phenylalanine*/blood ; Phenylalanine*/Phenylalanine*/Phenylalanine*/chemistry; Dietary Proteins/Dietary Proteins/Dietary Proteins/*administration & dosage

  • Source: Nutrients [Nutrients] 2021 Feb 02; Vol. 13 (2). Date of Electronic Publication: 2021 Feb 02.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Improved Eating Behaviour and Nutrient Intake in Noncompliant Patients with Phenylketonuria after Reintroducing a Protein Substitute: Observations from a Multicentre Study.

  • Authors : Green B; Medical Affairs, Nutricia Advanced Medical Nutrition, Wiltshire, BA14 0XQ, UK. .; Rahman Y

Subjects: Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*psychology ; Dietary Proteins/Dietary Proteins/Dietary Proteins/*administration & dosage ; Feeding Behavior/Feeding Behavior/Feeding Behavior/*psychology

  • Source: Nutrients [Nutrients] 2019 Aug 30; Vol. 11 (9). Date of Electronic Publication: 2019 Aug 30.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Report

Management of three preterm infants with phenylketonuria.

  • Authors : Weiss K; Dr. von Hauner Children's Hospital, Department of Inborn Errors of Metabolism, Ludwig-Maximilians-University, Munich, Germany.; Lotz-Havla A

Subjects: Dietary Proteins/Dietary Proteins/Dietary Proteins/*administration & dosage ; Enteral Nutrition/Enteral Nutrition/Enteral Nutrition/*methods ; Infant, Premature, Diseases/Infant, Premature, Diseases/Infant, Premature, Diseases/*therapy

  • Source: Nutrition (Burbank, Los Angeles County, Calif.) [Nutrition] 2020 Mar; Vol. 71, pp. 110619. Date of Electronic Publication: 2019 Oct 17.Publisher: Elsevier Science Country of Publication: United States NLM ID: 8802712 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Special Low Protein Foods Prescribed in England for PKU Patients: An Analysis of Prescribing Patterns and Cost.

  • Authors : Wood G; Faculty of Health, Education & Life Sciences, Birmingham City University, City South Campus, Westbourne Road, Edgbaston, Birmingham B15 3TN, UK.; Pinto A

Subjects: Diet, Protein-Restricted*/Diet, Protein-Restricted*/Diet, Protein-Restricted*/economics ; Practice Patterns, Physicians'*; Dietary Proteins/Dietary Proteins/Dietary Proteins/*analysis

  • Source: Nutrients [Nutrients] 2021 Nov 08; Vol. 13 (11). Date of Electronic Publication: 2021 Nov 08.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Dietary protein and protein substitute requirements in adults with phenylketonuria: A review of the clinical guidelines.

  • Authors : Firman S; Department of Nutritional Sciences, King's College London, London, United Kingdom; Department of Nutrition and Dietetics, Guy's and St Thomas' NHS Foundation Trust, London, United Kingdom

Subjects: Food, Formulated* ; Nutrition Policy*; Amino Acids/Amino Acids/Amino Acids/*administration & dosage

  • Source: Clinical nutrition (Edinburgh, Scotland) [Clin Nutr] 2021 Mar; Vol. 40 (3), pp. 702-709. Date of Electronic Publication: 2020 Nov 11.Publisher: Elsevier Country of Publication: England NLM ID: 8309603 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1532-1983

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Academic Journal

Protein Labelling Accuracy for UK Patients with PKU Following a Low Protein Diet.

  • Authors : Kraleva D; Faculty of Health, Education & Life Sciences, Birmingham City University City South Campus, Westbourne Road, Edgbaston, Birmingham B15 3TN, UK.; Evans S

Subjects: Diet, Gluten-Free/Diet, Gluten-Free/Diet, Gluten-Free/*standards ; Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*standards ; Dietary Proteins/Dietary Proteins/Dietary Proteins/*analysis

  • Source: Nutrients [Nutrients] 2020 Nov 10; Vol. 12 (11). Date of Electronic Publication: 2020 Nov 10.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

A 3 Year Longitudinal Prospective Review Examining the Dietary Profile and Contribution Made by Special Low Protein Foods to Energy and Macronutrient Intake in Children with Phenylketonuria.

  • Authors : Daly A; Dietetic Department, Birmingham Children's Hospital, Steelhouse Lane, Birmingham B4 6NH, UK.; Evans S

Subjects: Diet, Protein-Restricted* ; Foods, Specialized*/Foods, Specialized*/Foods, Specialized*/analysis ; Nutritive Value*

  • Source: Nutrients [Nutrients] 2020 Oct 15; Vol. 12 (10). Date of Electronic Publication: 2020 Oct 15.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Fifteen years of using a second stage protein substitute for weaning in phenylketonuria: a retrospective study.

  • Authors : Evans S; Dietetic Department, Birmingham Children's Hospital, Birmingham, UK.; Daly A

Subjects: Dietary Supplements* ; Weaning*; Diet/Diet/Diet/*methods

  • Source: Journal of human nutrition and dietetics : the official journal of the British Dietetic Association [J Hum Nutr Diet] 2018 Jun; Vol. 31 (3), pp. 349-356. Date of Electronic Publisher: Wiley on behalf of The British Dietetic Association Ltd., [c1988- Country of Publication: England NLM ID: 8904840 Publication Model:

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Academic Journal

An Observational Study Evaluating the Introduction of a Prolonged-Release Protein Substitute to the Dietary Management of Children with Phenylketonuria.

  • Authors : MacDonald A; Dietetic Department, Birmingham Women's and Children's Hospital, Steelhouse Lane, Birmingham B4 6NH, UK.; Ashmore C

Subjects: Dietary Proteins*; Phenylketonurias/Phenylketonurias/Phenylketonurias/*diet therapy ; Proteins/Proteins/Proteins/*administration & dosage

  • Source: Nutrients [Nutrients] 2020 Sep 03; Vol. 12 (9). Date of Electronic Publication: 2020 Sep 03.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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