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Academic Journal

Adaptation and Validation of a Questionnaire to Evaluate Knowledge of the Low Phe Diet in PKU.

  • Authors : Ramos-Álvarez R; Department of Social Psychology, Melilla Campus, Granada University, 52005 Melilla, Spain.; Kapp M

Subjects: Health Knowledge, Attitudes, Practice*; Diet Surveys/Diet Surveys/Diet Surveys/*standards ; Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*psychology

  • Source: Nutrients [Nutrients] 2021 Aug 07; Vol. 13 (8). Date of Electronic Publication: 2021 Aug 07.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

The Impact of the Use of Glycomacropeptide on Satiety and Dietary Intake in Phenylketonuria.

  • Authors : Daly A; Dietetic Department, Birmingham Children's Hospital, Steelhouse Lane, Birmingham B4 6NH, UK.; Evans S

Subjects: Amino Acids/Amino Acids/Amino Acids/*administration & dosage ; Caseins/Caseins/Caseins/*administration & dosage ; Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*methods

  • Source: Nutrients [Nutrients] 2020 Sep 04; Vol. 12 (9). Date of Electronic Publication: 2020 Sep 04.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Everyday Life, Dietary Practices, and Health Conditions of Adult PKU Patients: A Multicenter, Cross-Sectional Study.

  • Authors : Klimek A; Villa Metabolica, Department of Pediatric and Adolescent Medicine, University Medical Center Mainz, Mainz, Germany.; Baerwald C

Subjects: Quality of Life*; Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*statistics & numerical data ; Feeding Behavior/Feeding Behavior/Feeding Behavior/*psychology

  • Source: Annals of nutrition & metabolism [Ann Nutr Metab] 2020; Vol. 76 (4), pp. 251-258. Date of Electronic Publication: 2020 Sep 30.Publisher: Karger Country of Publication: Switzerland NLM ID: 8105511 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1421-9697

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Academic Journal

Improved Eating Behaviour and Nutrient Intake in Noncompliant Patients with Phenylketonuria after Reintroducing a Protein Substitute: Observations from a Multicentre Study.

  • Authors : Green B; Medical Affairs, Nutricia Advanced Medical Nutrition, Wiltshire, BA14 0XQ, UK. .; Rahman Y

Subjects: Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*psychology ; Dietary Proteins/Dietary Proteins/Dietary Proteins/*administration & dosage ; Feeding Behavior/Feeding Behavior/Feeding Behavior/*psychology

  • Source: Nutrients [Nutrients] 2019 Aug 30; Vol. 11 (9). Date of Electronic Publication: 2019 Aug 30.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Biomarkers of Micronutrients in Regular Follow-Up for Tyrosinemia Type 1 and Phenylketonuria Patients.

  • Authors : van Vliet K; Division of Metabolic Diseases, Groningen, Beatrix Children's Hospital, University Medical Center Groningen, University of Groningen, 9700 RB Groningen, The Netherlands.; Rodenburg IL

Subjects: Diet, Protein-Restricted*/Diet, Protein-Restricted*/Diet, Protein-Restricted*/adverse effects ; Dietary Supplements*/Dietary Supplements*/Dietary Supplements*/adverse effects ; Nutritional Status*

  • Source: Nutrients [Nutrients] 2019 Aug 27; Vol. 11 (9). Date of Electronic Publication: 2019 Aug 27.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Special Low Protein Foods Prescribed in England for PKU Patients: An Analysis of Prescribing Patterns and Cost.

  • Authors : Wood G; Faculty of Health, Education & Life Sciences, Birmingham City University, City South Campus, Westbourne Road, Edgbaston, Birmingham B15 3TN, UK.; Pinto A

Subjects: Diet, Protein-Restricted*/Diet, Protein-Restricted*/Diet, Protein-Restricted*/economics ; Practice Patterns, Physicians'*; Dietary Proteins/Dietary Proteins/Dietary Proteins/*analysis

  • Source: Nutrients [Nutrients] 2021 Nov 08; Vol. 13 (11). Date of Electronic Publication: 2021 Nov 08.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Provision and Supervision of Food and Protein Substitute in School for Children with PKU: Parent Experiences.

  • Authors : Jones H; Faculty of Health, Education & Life Sciences, Birmingham City University: City South Campus, Westbourne Road, Edgbaston, Birmingham B15 3TN, UK.; Pinto A

Subjects: Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*psychology ; Food Services/Food Services/Food Services/*organization & administration ; Parents/Parents/Parents/*psychology

  • Source: Nutrients [Nutrients] 2021 Oct 28; Vol. 13 (11). Date of Electronic Publication: 2021 Oct 28.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Metabolic Control of Patients with Phenylketonuria in a Portuguese Metabolic Centre Comparing Three Different Recommendations.

  • Authors : Kanufre V; Centro de Genética Médica, Centro Hospitalar Universitário do Porto (CHUPorto), 4099-028 Porto, Portugal.; Centro de Referência na Área de Doenças Hereditárias do Metabolismo, Centro Hospitalar Universitário do Porto-CHUPorto, 4099-001 Porto, Portugal.

Subjects: Biopterins/Biopterins/Biopterins/*analogs & derivatives ; Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*methods ; Phenylalanine/Phenylalanine/Phenylalanine/*blood

  • Source: Nutrients [Nutrients] 2021 Sep 06; Vol. 13 (9). Date of Electronic Publication: 2021 Sep 06.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

Exploring Drivers of Liking of Low-Phenylalanine Products in Subjects with Phenyilketonuria Using Check-All-That-Apply Method.

  • Authors : Proserpio C; Department of Food, Environmental and Nutritional Sciences (DeFENS), University of Milan, 20133 Milan, Italy. .; Pagliarini E

Subjects: Diet, Protein-Restricted*/Diet, Protein-Restricted*/Diet, Protein-Restricted*/adverse effects ; Dietary Supplements*/Dietary Supplements*/Dietary Supplements*/adverse effects ; Food Preferences*

  • Source: Nutrients [Nutrients] 2018 Aug 28; Vol. 10 (9). Date of Electronic Publication: 2018 Aug 28.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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Academic Journal

The Use of Glycomacropeptide in Patients with Phenylketonuria: A Systematic Review and Meta-Analysis.

  • Authors : Pena MJ; Departamento de Biomedicina, Unidade de Bioquímica, Faculdade de Medicina, Universidade do Porto, 4200-319 Porto, Portugal. .; Pinto A

Subjects: Dietary Supplements*; Caseins/Caseins/Caseins/*administration & dosage ; Diet, Protein-Restricted/Diet, Protein-Restricted/Diet, Protein-Restricted/*methods

  • Source: Nutrients [Nutrients] 2018 Nov 18; Vol. 10 (11). Date of Electronic Publication: 2018 Nov 18.Publisher: MDPI Publishing Country of Publication: Switzerland NLM ID: 101521595 Publication Model: Electronic Cited Medium: Internet ISSN:

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