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Academic Journal

Renal and Extra Renal Manifestations in Adult Zebrafish Model of Cystinosis.

  • Authors : Berlingerio SP; Laboratory of Pediatric Nephrology, KU Leuven, 3000 Leuven, Belgium.; He J

Subjects: Disease Models, Animal* ; Mutation*; Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*metabolism

  • Source: International journal of molecular sciences [Int J Mol Sci] 2021 Aug 30; Vol. 22 (17). Date of Electronic Publication: 2021 Aug 30.Publisher: MDPI Country of Publication: Switzerland NLM ID: 101092791 Publication Model: Electronic Cited Medium: Internet ISSN: 1422-0067

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Academic Journal

Tissue distribution, hormonal regulation, ontogeny, diurnal expression, and induction of mouse cystine transporters Slc3a1 and Slc7a9.

  • Authors : Wu KC; Department of Pharmacology, Toxicology and Therapeutics, School of Medicine, University of Kansas, Kansas City, MO, USA.; Reisman SA

Subjects: Amino Acid Transport Systems, Basic/Amino Acid Transport Systems, Basic/Amino Acid Transport Systems, Basic/*metabolism ; Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*metabolism ; Cystine/Cystine/Cystine/*metabolism

  • Source: Free radical research [Free Radic Res] 2020 Jul; Vol. 54 (7), pp. 525-534. Date of Electronic Publication: 2020 Sep 01.Publisher: Informa Healthcare Country of Publication: England NLM ID: 9423872 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Cystinosin-LKG rescues cystine accumulation and decreases apoptosis rate in cystinotic proximal tubular epithelial cells.

  • Authors : Taranta A; Department of Nephrology and Urology, Division of Nephrology, Bambino Gesù Children's Hospital and Research Institute, Rome, Italy.; Bellomo F

Subjects: Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*metabolism ; Cystine/Cystine/Cystine/*metabolism ; Cystinosis/Cystinosis/Cystinosis/*metabolism

  • Source: Pediatric research [Pediatr Res] 2017 Jan; Vol. 81 (1-1), pp. 113-119. Date of Electronic Publication: 2016 Sep 22.Publisher: Nature Publishing Group Country of Publication: United States NLM ID: 0100714 Publication Model: Print-Electronic Cited Medium: Internet

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Academic Journal

Cystine import is a valuable but risky process whose hazards Escherichia coli minimizes by inducing a cysteine exporter.

  • Authors : Korshunov S; Department of Microbiology, University of Illinois, Urbana, IL, 61801, USA.; Imlay KRC

Subjects: Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*metabolism ; Cystine/Cystine/Cystine/*metabolism ; Escherichia coli/Escherichia coli/Escherichia coli/*metabolism

  • Source: Molecular microbiology [Mol Microbiol] 2020 Jan; Vol. 113 (1), pp. 22-39. Date of Electronic Publication: 2019 Nov 11.Publisher: Blackwell Scientific Publications Country of Publication: England NLM ID: 8712028 Publication Model: Print-Electronic Cited Medium: Internet

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Academic Journal

The novel aminoglycoside, ELX-02, permits CTNSW138X translational read-through and restores lysosomal cystine efflux in cystinosis.

  • Authors : Brasell EJ; McGill University, Department of Human Genetics, Montreal, Canada.; Chu LL

Subjects: Mutation*; Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*physiology ; Aminoglycosides/Aminoglycosides/Aminoglycosides/*pharmacology

  • Source: PloS one [PLoS One] 2019 Dec 04; Vol. 14 (12), pp. e0223954. Date of Electronic Publication: 2019 Dec 04 (Print Publication: 2019).Publisher: Public Library of Science Country of Publication: United States NLM ID: 101285081 Publication Model: eCollection Cited Medium: Internet

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Academic Journal

A deletion in the Ctns gene causes renal tubular dysfunction and cystine accumulation in LEA/Tohm rats.

  • Authors : Shimizu Y; Department of Laboratory Animal Medicine, Research Institute, National Center for Global Health and Medicine (NCGM), 1-21-1 Toyama, Shinjyuku-ku, Tokyo, 162-8655, Japan.; Department of Pediatrics and Adolescent Medicine, Juntendo University Graduate School of Medicine, 2-1-1 Hongo, Bunkyo-ku, Tokyo, 113-8421, Japan.

Subjects: Sequence Deletion*; Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*genetics ; Cystine/Cystine/Cystine/*metabolism

  • Source: Mammalian genome : official journal of the International Mammalian Genome Society [Mamm Genome] 2019 Feb; Vol. 30 (1-2), pp. 23-33. Date of Electronic Publication: 2018 Dec 27.Publisher: Springer-Verlag Country of Publication: United States NLM ID: 9100916 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Stem cell microvesicles transfer cystinosin to human cystinotic cells and reduce cystine accumulation in vitro.

  • Authors : Iglesias DM; Department of Pediatrics, Montreal Children's Hospital Research Institute, McGill University, Montréal, Québec, Canada.; El-Kares R

Subjects: Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*metabolism ; Cystine/Cystine/Cystine/*metabolism ; Cystinosis/Cystinosis/Cystinosis/*metabolism

  • Source: PloS one [PLoS One] 2012; Vol. 7 (8), pp. e42840. Date of Electronic Publication: 2012 Aug 13.Publisher: Public Library of Science Country of Publication: United States NLM ID: 101285081 Publication Model: Print-Electronic Cited Medium: Internet

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Academic Journal

Transcriptional and posttranscriptional regulation of the CTNS gene.

  • Authors : Corallini S; Division of Nephrology and Dialysis, Bambino Gesù Children's Hospital and Research Institute, 00165 Rome, Italy.; Taranta A

Subjects: Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*metabolism ; Cystine/Cystine/Cystine/*metabolism ; Gene Expression Regulation/Gene Expression Regulation/Gene Expression Regulation/*physiology

  • Source: Pediatric research [Pediatr Res] 2011 Aug; Vol. 70 (2), pp. 130-5.Publisher: Nature Publishing Group Country of Publication: United States NLM ID: 0100714 Publication Model: Print Cited Medium: Internet ISSN:

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Academic Journal

Quantitative in vivo and ex vivo confocal microscopy analysis of corneal cystine crystals in the Ctns knockout mouse.

  • Authors : Simpson J; Department of Biochemistry, Jawaharlal Nehru Medical College, Maharashtra, India. ; Nien CJ

Subjects: Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*deficiency ; Cicatrix/Cicatrix/Cicatrix/*pathology ; Cornea/Cornea/Cornea/*pathology Cystinosis, ocular nonnephropathic

  • Source: Molecular vision [Mol Vis] 2011; Vol. 17, pp. 2212-20. Date of Electronic Publication: 2011 Aug 17.Publisher: Molecular Vision Country of Publication: United States NLM ID: 9605351 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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Academic Journal

Evaluation of topical cysteamine therapy in the CTNS(-/-) knockout mouse using in vivo confocal microscopy.

  • Authors : Simpson JL; Gavin Herbert Eye Institute, University of California Irvine, Irvine, CA 92697-4375, USA. ; Nien CJ

Subjects: Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/Amino Acid Transport Systems, Neutral/*deficiency ; Cornea/Cornea/Cornea/*metabolism ; Cysteamine/Cysteamine/Cysteamine/*administration & dosage

  • Source: Molecular vision [Mol Vis] 2011; Vol. 17, pp. 2649-54. Date of Electronic Publication: 2011 Oct 08.Publisher: Molecular Vision Country of Publication: United States NLM ID: 9605351 Publication Model: Print-Electronic Cited Medium: Internet ISSN:

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  • 1-10 of  42 results for ""Amino Acid Transport Systems, Neutral""