Biliary atresia with splenic malformation with associated ductal plate malformation and duodenal atresia: A case report.

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  • Additional Information
    • Source:
      Publisher: Medknow Country of Publication: India NLM ID: 7605904 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 0974-5130 (Electronic) Linking ISSN: 03774929 NLM ISO Abbreviation: Indian J Pathol Microbiol Subsets: MEDLINE
    • Publication Information:
      Publication: Mumbai : Medknow
      Original Publication: Chandigarh : Indian Association of Pathologists & Microbiologists.
    • Subject Terms:
      Biliary Atresia*/complications ; Biliary Atresia*/surgery ; Biliary Atresia*/diagnosis ; Duodenal Obstruction*/surgery ; Duodenal Obstruction*/diagnostic imaging ; Intestinal Atresia*/surgery ; Spleen*/abnormalities ; Spleen*/diagnostic imaging ; Spleen*/pathology; Humans ; Infant ; Fatal Outcome
    • Abstract:
      Abstract: Biliary atresia (BA) is the most common cause of the obstructive type of neonatal cholestasis that requires prompt surgical intervention. About 10% of neonates with BA have other congenital anomalies, of which splenic malformation (BASM) is a well-known distinct sub-group. There is sparse literature on the association of duodenal atresia and ductal plate malformation (DPM) in patients of BASM. We describe a BASM associated with DPM and duodenal atresia in a 35-day-old infant, who succumbed at 40 days, before portoenterostomy could be performed. Duodenal atresia can be one of the associated malformations associated with BASM and ductal plate abnormalities. In our case, the child did not survive.
      (Copyright © 2023 Indian Journal of Pathology and Microbiology.)
    • References:
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    • Subject Terms:
      Familial duodenal atresia
    • Publication Date:
      Date Created: 20240223 Date Completed: 20241206 Latest Revision: 20250103
    • Publication Date:
      20250103
    • Accession Number:
      10.4103/ijpm.ijpm_182_23
    • Accession Number:
      38394407