Hemangioblastoma masquerading as a ring enhancing lesion in the cerebellum: A case report.

Publisher: Lippincott Williams & Wilkins Country of Publication: United States NLM ID: 2985248R Publication Model: Print Cited Medium: Internet ISSN: 1536-5964 (Electronic) Linking ISSN: 00257974 NLM ISO Abbreviation: Medicine (Baltimore) Subsets: MEDLINE

Original Publication: Hagerstown, Md : Lippincott Williams & Wilkins

Cerebellar Neoplasms/*diagnosis ; Cerebellum/*diagnostic imaging ; Headache/*etiology ; Hemangioblastoma/*diagnosis ; Optic Nerve Diseases/*etiology; Adult ; Cerebellar Neoplasms/surgery ; Computed Tomography Angiography ; Female ; Hemangioblastoma/surgery ; Humans ; Magnetic Resonance Imaging ; Tomography, X-Ray Computed

Rationale: Hemangioblastomas (HGBMs) are very rare, and the cerebellum is usually the most common site of occurrence. HGBMs with ring-enhanced walls are often misdiagnosed as metastases, abscesses, glioblastomas, tuberculomas, and demyelinating diseases. Thus, we present a rare case of HGBM masquerading as a ring-enhancing lesion in the cerebellum.
Patient Concerns: We present a 33-year-old female who was admitted to our department because of headaches, unstable walking, and visual loss in both eyes. Cranial nerve examination revealed deficits in cranial nerve II.
Diagnosis: Magnetic resonance imaging revealed 2 cystic lesions in the cerebellum, with irregular ring-enhanced cyst walls composed of smaller nodular parts. Immunohistochemical staining of resected specimens established HGBM.
Interventions: The lesions were completely resected using a right retrosigmoid approach.
Outcomes: Two years of follow-up revealed no recurrence of her symptoms or tumor. She is currently well and performs her daily duties.
Lessons: HGBMs with enhanced cysts are often misdiagnosed by radiology because of their ring-enhanced nature. Computed tomography angiography may be the best modality for differentiating cerebellar HGBM from other ring-enhancing lesions. Surgery is the gold standard of treatment for these lesions.
Competing Interests: The authors have no funding and conflicts of interest to disclose.
(Copyright © 2022 the Author(s). Published by Wolters Kluwer Health, Inc.)

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Date Created: 20220121 Date Completed: 20220228 Latest Revision: 20230103

20231215

PMC8772639

10.1097/MD.0000000000028665

35060562