Isolated Left Subclavian Artery, Complete Atrioventricular Block, and Tricuspid Atresia in a Neonate.

Publisher: published in the Cardiovascular Surgical Research Laboratories, Texas Heart Institute Country of Publication: United States NLM ID: 8214622 Publication Model: eCollection Cited Medium: Internet ISSN: 1526-6702 (Electronic) Linking ISSN: 07302347 NLM ISO Abbreviation: Tex Heart Inst J Subsets: MEDLINE

Original Publication: Houston, TX : published in the Cardiovascular Surgical Research Laboratories, Texas Heart Institute, c1982-

Abnormalities, Multiple*; Atrioventricular Block/*congenital ; Heart Block/*congenital ; Subclavian Artery/*abnormalities ; Tricuspid Atresia/*complications ; Vascular Malformations/*complications; Atrioventricular Block/diagnosis ; Atrioventricular Block/surgery ; Cardiac Pacing, Artificial ; Computed Tomography Angiography ; Echocardiography, Doppler, Color ; Equipment Design ; Female ; Fontan Procedure ; Gestational Age ; Heart Block/diagnosis ; Heart Block/surgery ; Humans ; Infant, Newborn ; Infant, Premature ; Pacemaker, Artificial ; Pulmonary Artery/abnormalities ; Pulmonary Artery/diagnostic imaging ; Replantation ; Subclavian Artery/diagnostic imaging ; Subclavian Artery/surgery ; Treatment Outcome ; Tricuspid Atresia/diagnostic imaging ; Tricuspid Atresia/surgery ; Vascular Malformations/diagnostic imaging ; Vascular Malformations/surgery

Isolated left subclavian artery is one of the rarer aortic arch anomalies. It has been associated with other congenital heart diseases, typically tetralogy of Fallot, double-outlet right ventricle, and atrial and ventricular septal defects. Its significant clinical implications include a left-to-right shunt from the vertebrobasilar system, which causes pulmonary overcirculation and subclavian steal. We present an unusual case of a premature infant who was diagnosed prenatally with congenital complete atrioventricular block and tricuspid atresia and was found to have an isolated left subclavian artery postnatally. The patient underwent implantation of a permanent single-chamber epicardial pacing system. To our knowledge, this combination of lesions has not been reported-and in our case, it influenced our surgical planning.

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Keywords: Abnormalities, multiple/diagnosis/surgery; aortic arch syndromes/complications; atrioventricular block/complications/diagnosis/etiology; ductus arteriosus/complications; heart defects, congenital/complications/surgery; infant, newborn; prenatal diagnosis; subclavian artery/abnormalities; subclavian steal syndrome/diagnosis/etiology/pathology; tricuspid atresia/diagnosis

Congenital heart block

Date Created: 20170120 Date Completed: 20170905 Latest Revision: 20181113

20240829

PMC5179167

10.14503/THIJ-15-5692

28100981