Encefalopatía epiléptica infantil temprana. Descripción de un caso de síndrome de Ohtahara. (Spanish)

A case of epileptic encephalopathy. The Ohtahara syndrome. (English)

Ohtahara syndrome is included in the group of epileptic encephalopathies of infancy and is characterized by convulsive disease with early appearance of epileptic seizures specially tonic and myoclonic type, having an special electroencephalographic pattern of "Burst-Suppression". We describe a clinical case in a female infant with congenital cardiopathy and neurological affection of periventricular leukomalacia, with no response to treatment, that progressed to status epileptic and who finally died at 4 months of age. [ABSTRACT FROM AUTHOR]

El síndrome de Ohtahara es una enfermedad paroxística convulsiva perteneciente al grupo de encefalopatías epilépticas de la infancia de aparición temprana, caracterizada clínicamente por espasmos tónicos y convulsiones mioclónicas. Tiene un especial patrón electroencefalográfico de "paroxismo-supresión". Presentamos el caso clínico de una lactante con cardiopatía congénita y afección neurológica de leucomalacia periventricular, sin respuesta al tratamiento y evolución hacia estado epiléptico que finalmente falleció a los 4 meses de edad. [ABSTRACT FROM AUTHOR]

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